Mueller E B, Niethammer K, Rees D, Partsch C J
Klinikum Esslingen, Paediatric Hospital, Esslingen, Germany.
Klin Padiatr. 2009 Sep;221(5):308-9. doi: 10.1055/s-0029-1234077. Epub 2009 Aug 25.
This article is about a 9-year-old boy with known homozygous sickle cell disease who developed unilateral exophthalmia and eyelid swelling during a sickle cell crisis. The symptoms were due to a vaso-occlusive event in the orbital bones,known as orbital compression syndrome, which is a rare complication of sickle cell disease.
本文讲述的是一名患有已知纯合子镰状细胞病的9岁男孩,在镰状细胞危象期间出现了单侧眼球突出和眼睑肿胀。这些症状是由于眼眶骨发生血管阻塞事件,即眼眶压迫综合征,这是镰状细胞病的一种罕见并发症。