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一名16岁男孩以颈部淋巴结病为表现的多发性骨髓瘤。

Multiple myeloma presenting as cervical lymphadenopathy in a 16-year-old boy.

作者信息

Brady-West Doreen C, Buchner-Daley Loretta M, McGrowder Donovan A, Taylor-Houston Joye, West Kamille A

机构信息

Department of Pathology, Faculty of Medical Sciences, University of the West Indies, Mona, Kingston, Jamaica.

出版信息

J Natl Med Assoc. 2009 Aug;101(8):810-2. doi: 10.1016/s0027-9684(15)31012-9.

DOI:10.1016/s0027-9684(15)31012-9
PMID:19715046
Abstract

A 16-year-old boy presented with cervical lymphadenopathy and histological features of a plasmacytoma. He was found to have lytic bone lesions, a serum IgA M-protein, and elevated beta 2-microglobulin. There was absence of anemia, hypercalcemia, and marrow plasmacytosis. He received local irradiation and 6 courses of chemotherapy comprising vincristine, adriamycin, and dexamethasone given at 4 weekly intervals. This was followed by complete resolution of his disease, and he remains clinically well 5 years after completion of therapy.

摘要

一名16岁男孩出现颈部淋巴结病及浆细胞瘤的组织学特征。他被发现有溶骨性骨病变、血清IgA M蛋白以及β2微球蛋白升高。不存在贫血、高钙血症和骨髓浆细胞增多症。他接受了局部放疗以及6个疗程的化疗,化疗方案为长春新碱、阿霉素和地塞米松,每4周给药一次。之后他的疾病完全缓解,在完成治疗5年后临床状况良好。

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