Singal Arbinder Kumar, Chandrasekharam V V S S
MGM's New Bombay Hospital, Vashi and MGM University of Health Sciences, Navi Mumbai 400703, India.
Pediatr Surg Int. 2009 Dec;25(12):1117-21. doi: 10.1007/s00383-009-2470-3. Epub 2009 Sep 2.
Congenital primary bladder diverticulum is a rare condition and may present with urinary infection; other forms of presentation are rare. We present a series of infants who presented with urinary retention secondary to large primary bladder diverticulum.
Seven infants were evaluated for symptoms of lower urinary tract obstruction. All seven were infant boys; three were neonates. Investigations included ultrasonogram, voiding cystourethrogram (VCUG) and cystoscopy.
Six infants had single large diverticulum while one had bilateral diverticula. VCUG was diagnostic in all cases demonstrating the mechanism of obstruction clearly except one where bilateral diverticula was diagnosed only on cystoscopy prior to definitive surgery. Five children (including one neonate) underwent successful definitive repair consisting of diverticulectomy and ureteral re-implant while two neonates were planned for a staged correction. One neonate later in the series underwent definitive primary repair as bladder was good sized. All five children have done well after definitive repair at a follow-up of 6-72 months.
Primary bladder diverticulum in infants may present with lower urinary obstructive symptoms indistinguishable from posterior urethral valves. A carefully done VCUG can help in diagnosis. Primary definitive repair can be undertaken even in first few months of life with good results.
先天性原发性膀胱憩室是一种罕见疾病,可能表现为泌尿系统感染;其他表现形式较为罕见。我们报告了一系列因巨大原发性膀胱憩室继发尿潴留的婴儿病例。
对7名有下尿路梗阻症状的婴儿进行评估。所有7名均为男婴;3名是新生儿。检查包括超声检查、排尿性膀胱尿道造影(VCUG)和膀胱镜检查。
6名婴儿有单个巨大憩室,1名有双侧憩室。除1例双侧憩室仅在确定性手术前行膀胱镜检查时确诊外,VCUG在所有病例中均具有诊断价值,能清晰显示梗阻机制。5名儿童(包括1名新生儿)成功接受了包括憩室切除术和输尿管再植术的确定性修复,2名新生儿计划分期矫正。该系列中的1名新生儿后来因膀胱大小合适接受了确定性一期修复。所有5名儿童在确定性修复后的6至72个月随访中情况良好。
婴儿原发性膀胱憩室可能表现出与后尿道瓣膜难以区分的下尿路梗阻症状。仔细进行的VCUG有助于诊断。即使在生命的最初几个月也可进行原发性确定性修复,效果良好。