成人肾母细胞瘤。

Adult Wilms' tumor.

作者信息

Sharma Mriganka S, Ahmed Mufiz Z

机构信息

Department of General Surgery, GTB Hospital, Dilshad Garden, Delhi, India.

出版信息

Saudi J Kidney Dis Transpl. 2009 Sep;20(5):835-7.

PMID:19736484

Abstract

Adult Wilms' Tumor (AWT) is a rare entity arising from the metanephric blastema. There are only about 200 cases reported in world literature. The staging of AWT is done in the same way as in children according to the National Wilms' Tumour Stage Group (NWTSG). Definitive treatment plans for AWT are undefined but surgical treatment has the highest priority. There is also consensus on the need for multimodality approach. We report a case of AWT who remains disease free, three years after undergoing multimodality treatment.

摘要

成人威尔姆斯瘤（AWT）是一种起源于后肾胚基的罕见疾病。世界文献中仅报道了约200例病例。AWT的分期与儿童一样，根据国家威尔姆斯瘤分期小组（NWTSG）进行。AWT的明确治疗方案尚未确定，但手术治疗具有最高优先级。对于多模式治疗方法的必要性也存在共识。我们报告了一例AWT患者，在接受多模式治疗三年后仍无疾病。