Aniba K, Ghannane H, Lmejjati M, Ouali M, Jalal H, Ousehal A, Ait Benali S
Service de neurochirurgie, CHU Mohamed VI, poste Allal El Fassi, Marrakech, Morocco.
Arch Pediatr. 2009 Nov;16(11):1467-9. doi: 10.1016/j.arcped.2009.07.024. Epub 2009 Sep 11.
Sacrococcygeal teratomas are rare congenital tumors, generally discovered at birth. These tumors are seldom observed in children. Radical resection must be performed to avoid potentially malignant recurrence even if the primary lesion is benign. We report a case in an 8-year-old girl who did not have a past medical history. Since the age of 2 years, she presented a progressive sacral tumefaction with no neurological deficit. The MRI showed a large sacrococcygeal cyst in hypointense-signal T1-weighted imaging with no contrast enhancement, and a hyperintense signal in T2-weighted imaging. At surgery, the tumor was totally removed. The intraoperative aspect was that of a viscous cyst. The histological study showed a sacrococcygeal teratoma.
骶尾部畸胎瘤是一种罕见的先天性肿瘤，通常在出生时被发现。这些肿瘤在儿童中很少见。即使原发性病变是良性的，也必须进行根治性切除以避免潜在的恶性复发。我们报告一例8岁女童病例，该女童既往无病史。自2岁起，她出现进行性骶部肿胀，无神经功能缺损。MRI显示在T1加权成像中为低信号的巨大骶尾部囊肿，无对比增强，在T2加权成像中为高信号。手术中，肿瘤被完全切除。术中所见为一个粘性囊肿。组织学研究显示为骶尾部畸胎瘤。
