Al-Khaldi Abdulaziz, Alharbi Abdulmohsen, Tamimi Omar, Mohammed Yasser
Division of Cardiac Surgery, King Abdulaziz Medical City, Riyadh, Saudi Arabia.
Ann Thorac Surg. 2009 Oct;88(4):1343-5. doi: 10.1016/j.athoracsur.2009.02.020.
The outcomes of surgical repair for diffuse pulmonary artery stenoses due to arterial tortuosity syndrome are unknown. We report a 1-year-old girl with tortuosity syndrome who presented with suprasystemic right ventricular pressure due to distortion and stenoses of the pulmonary artery branches. We describe the operative findings of this unique pathology and the surgical techniques used to completely reconstruct the pulmonary arterial tree, with normalization of the right ventricular pressure.
动脉迂曲综合征所致弥漫性肺动脉狭窄的手术修复结果尚不清楚。我们报告一名患有迂曲综合征的1岁女孩，因肺动脉分支扭曲和狭窄出现右心室压力高于体循环压力。我们描述了这种独特病理情况的手术发现以及用于完全重建肺动脉树并使右心室压力恢复正常的手术技术。
