Mićović S, Djukanović B, Milojević P, Nezić D, Jović M, Jovović Lj, Tomić S, Lausević-Vuk Lj
Institut za kardiovaskularne bolesti "Dedinje", Beograd.
Acta Chir Iugosl. 2009;56(2):97-9. doi: 10.2298/aci0902097m.
Quadricuspid aortic valve is rare congenital anomaly. There are only 197 cases published in literature so far. That includes clinical and autopsy reports. This congenital anomaly occurs more often in pulmonary valve but function stays normal in 10 of lies. On the other side, in aortic position valve is malfunctioning in 50% of cases. Valve regurgitation is more likely to occur than stenosis In this kind of malformation, valves are prone to early dysfunction and endocarditis due to different valve architecture and unequal distribution of mechanical stress along valve cusps. Aortic valve replacement is indicated in younger population of these patients. This is a case report of rare congenital anomaly of big blood vessels--aortic valve with four cusps. This anomaly produced significant aortic regurgitation so this patient was indicated for aortic valve replacement.
四叶式主动脉瓣是一种罕见的先天性异常。迄今为止,文献中仅发表了197例病例,其中包括临床和尸检报告。这种先天性异常在肺动脉瓣中更常见,但10%的病例功能保持正常。另一方面,在主动脉位置,50%的病例瓣膜功能异常。在这种畸形中,瓣膜反流比狭窄更易发生,由于瓣膜结构不同以及沿瓣膜尖的机械应力分布不均,瓣膜容易早期功能障碍和心内膜炎。对于这些患者中的年轻人群,建议进行主动脉瓣置换。这是一例关于大血管罕见先天性异常——四叶式主动脉瓣的病例报告。这种异常导致了严重的主动脉反流,因此该患者被建议进行主动脉瓣置换。