Jaiman Richa, Gangopadhyay Ajay N, Gupta Dinesh K, Srivastava Punit, Upadhyaya Vijay D, Sharma Shiv P, Kumar Vijayendra
Department of Surgery, SN Medical College, Agra-282005, Uttar Pradesh, India.
Cases J. 2009 Jul 23;2:7772. doi: 10.4076/1757-1626-2-7772.
The congenital constriction ring of lower extremity is very uncommon and rare condition. The actual incidence in general population is not known. In English literature, very few cases are reported time to time as congenital constriction band syndrome associated with musculoskeletal disorder like congenital talipes equino varus. The lesion can involve skin only or goes to deeper structure up to bone, which can lead to gangrene of foot or auto amputation.
We are presenting a case of bilateral congenital constriction ring in lower limb who presented at age of 4 year without any other associated congenital anomaly, simply managed by Z-plasty, which improves quality of life after physiotherapy.
Congenital constriction ring of lower limb is extremely rare condition in children. Early diagnosis and management is mandatory, either in single stage or by stage procedure, to prevent auto-amputation of limb and to improve quality of life on feet.
下肢先天性缩窄环是一种非常罕见的病症。一般人群中的实际发病率尚不清楚。在英文文献中，时有少量病例被报道为与先天性马蹄内翻足等肌肉骨骼疾病相关的先天性缩窄带综合征。该病变可仅累及皮肤，或深入至骨骼等更深层次结构，这可能导致足部坏疽或自行截肢。
我们报告一例4岁时就诊的双侧下肢先天性缩窄环病例，无任何其他相关先天性异常，单纯通过Z成形术治疗，经物理治疗后生活质量得到改善。
儿童下肢先天性缩窄环极为罕见。早期诊断和治疗至关重要，无论是一期手术还是分期手术，以防止肢体自行截肢并提高足部生活质量。
