Quinderé Lêda Bezerra, Cavalcante Roberta Barroso, Nonaka Cassiano Francisco Weege, Miguel Márcia Cristina da Costa, de Souza Lélia Batista
Pediatric Dentistry Department, Federal University of Rio Grande do Norte, Rio Grande do Norte, Brazil.
Quintessence Int. 2010 Jan;41(1):13-6.
Regional odontodysplasia is a rare developmental anomaly of the teeth that affects enamel and dentin. Its etiology is unknown, but the most accepted theory refers to circulatory disorders associated with vascular nevi. An uncommon case of regional odontodysplasia involving three quadrants of the jaws is reported. An 8-year-old boy was referred to the authors' institution with lack of teeth as a major symptom. There was no hereditary anomaly in the family. Extraoral examination revealed a brown discoloration on the skin on the right side of the face, neck, and chest. Detailed intraoral examination showed hypoplastic and carious teeth. Fistulae and gingival overgrowth were also observed. Radiographically, the affected teeth presented the pathognomonic image of "ghost teeth." Conservative treatment was instituted.
局部牙发育异常是一种罕见的牙齿发育异常，会影响牙釉质和牙本质。其病因尚不清楚，但最被广泛接受的理论认为与血管痣相关的循环系统紊乱有关。本文报告了一例罕见的累及颌骨三个象限的局部牙发育异常病例。一名8岁男孩因牙齿缺失作为主要症状被转诊至作者所在机构。家族中无遗传异常。口腔外检查发现面部右侧、颈部和胸部皮肤有褐色色素沉着。详细的口腔内检查显示牙齿发育不全且有龋齿。还观察到瘘管和牙龈增生。影像学检查显示，患牙呈现出“鬼牙”的典型影像。遂采取保守治疗。
