Schwartzenberg Shmuel, Sherez Jack, Wexler Dov, Aviram Galit, Keren Gad
Department of Cardiology, Tel Aviv Sourasky Medical Center, Tel Aviv, Israel.
Isr Med Assoc J. 2009 Jul;11(7):426-9.
Isolated ventricular non-compaction is a frequently underdiagnosed rare congenital cardiomyopathy. The importance of diagnosing this cardiomyopathy lies especially in asymptomatic patients, screening relatives of index cases in order to focus on their follow-up, and searching for criteria warranting prophylactic anticoagulation, implantable cardioverter defibrillator and anti-remodeling drugs such as angiotensin-converting inhibitors. We present the clinical and imaging characteristics of this entity and discuss some of the therapeutic dilemmas involving these patients.
孤立性心室肌致密化不全是一种常被漏诊的罕见先天性心肌病。诊断这种心肌病的重要性尤其体现在无症状患者身上，即筛查索引病例的亲属以便关注其随访情况，以及寻找有必要进行预防性抗凝、植入式心脏复律除颤器治疗和使用如血管紧张素转换酶抑制剂等抗重塑药物的标准。我们介绍了该疾病的临床和影像学特征，并讨论了涉及这些患者的一些治疗困境。
