Kułakowska Alina, Kapica-Topczewska Katarzyna, Borowik Helena, Drozdowski Wiesław
Uniwersytet Medyczny w Białymstoku, Klinika Neurologii.
Pol Merkur Lekarski. 2009 Oct;27(160):334-7.
Moyamoya disease is a rare, progressive disease of the vessels diagnosed according to characteristic abnormalities of brain arteries in the angiography. The incidence of moyamoya disease in Europe is lower than in Asia and its clinical course in European population is probably different from Asiatic (older age of onset and rare incidence of hemorrhagic strokes).
Two young patients were diagnosed as moyamoya disease on the basis of clinical symptoms (ischaemic stroke) and results of brain vessels' angiography, which documented an occlusion of both internal carotid arteries above branching-off the ocular arteries in the first patient and stenosis of distal internal carotid arteries and proximal medial and anterior cerebral arteries in the second one. Both patients are under control of the Neurological Outpatient Department and their neurological state is stable.
Despite that moyamoya disease is a rare cause of ischaemic stroke, it should be always considered as one of etiologic factors, especially in young patients.
烟雾病是一种罕见的、进行性血管疾病,根据血管造影中脑动脉的特征性异常进行诊断。欧洲烟雾病的发病率低于亚洲,其在欧洲人群中的临床病程可能与亚洲人不同(发病年龄较大且出血性中风发病率较低)。
两名年轻患者根据临床症状(缺血性中风)和脑血管造影结果被诊断为烟雾病,血管造影显示第一名患者双侧颈内动脉在眼动脉分支上方闭塞,第二名患者颈内动脉远端及大脑中动脉和大脑前动脉近端狭窄。两名患者均在神经科门诊接受治疗,神经状态稳定。
尽管烟雾病是缺血性中风的罕见病因,但应始终将其视为病因之一,尤其是在年轻患者中。