Kiatsoontorn Kraiyot, Takami Toshihiro, Ichinose Tsutomu, Chokyu Isao, Tsuyuguchi Naohiro, Ohsawa Masahiko, Ohata Kenji
Department of Neurosurgery, Osaka City University Graduate School of Medicine.
Neurol Med Chir (Tokyo). 2009 Nov;49(11):542-5. doi: 10.2176/nmc.49.542.
A 25-year-old male patient presented with an extremely rare primary spinal peripheral primitive neuroectodermal tumor (pPNET) manifesting as acutely progressive paraparesis and back pain. Neuroimaging and intraoperative examination showed that the tumor was confined to the epidural space of the thoracic spine. The patient was treated successfully by gross total resection of the tumor followed by chemotherapy and local radiotherapy. The present case illustrates the unexpected occurrence and important differential diagnosis of primary epidural pPNET of the thoracic spine in young patients presenting with progressive paraparesis and back pain.
一名25岁男性患者出现了极为罕见的原发性脊柱外周原始神经外胚层肿瘤(pPNET),表现为急性进行性双下肢轻瘫和背痛。神经影像学检查及术中检查显示,肿瘤局限于胸椎硬膜外间隙。通过肿瘤全切术,随后进行化疗和局部放疗,该患者得到了成功治疗。本病例说明了在出现进行性双下肢轻瘫和背痛的年轻患者中,胸椎原发性硬膜外pPNET的意外发生情况及重要的鉴别诊断。