Choulakian Mazen Yohanness, Williams H Bruce
Faculté de médecine et des sciences de la santé, Université de Sherbrooke, Sherbrooke, Quebec.
Can J Plast Surg. 2008 Winter;16(4):221-3. doi: 10.1177/229255030801600409.
Congenital constriction band syndrome is a sporadic condition that may also be present in association with other congenital anomalies. It has an incidence varying from one in 1200 to one in 15,000 live births. There is a significant predilection for the upper extremities and distal limbs. The two main objectives for the treatment of congenital constriction band syndrome are improvement of function and improvement of cosmetic appearance. Different surgical techniques, such as Z-plasty, have been described and used for decades; however, direct closure after the excision of the constricting band seems to be the simplest and most appropriate, allowing the fatty tissue to naturally reposition itself under the skin. This technique is used in a two-stage approach to avoid affecting distal circulation to the limb.
先天性束带综合征是一种散发性疾病，也可能与其他先天性异常同时存在。其发病率在每1200至15000例活产儿中出现1例。上肢和四肢远端明显受累。治疗先天性束带综合征的两个主要目标是改善功能和改善外观。诸如Z成形术等不同的手术技术已被描述并使用了数十年；然而，切除束带后直接缝合似乎是最简单且最合适的方法，可使脂肪组织自然地在皮下重新定位。该技术采用两阶段方法使用，以避免影响肢体远端循环。
