Cocchiara G, Romano M, Buscemi G, Lo Monte A I, Florena A M, Bartolotta T V, Taibbi A, Di Bernardo A, Di Paola P, Marazzo E, Agrusa A, Romano G
Department of Generaly Surgery of Uremic and Organ Transplantation, University of Palermo, Italy.
G Chir. 2009 Oct;30(10):422-5.
Primary malignant fibrous histiocytoma (MFH) is a rare and biologically aggressive tumor. Differential diagnosis must include cystic neoplasms of the pancreas (mucinous and serous cystoadenoma or cystocarcinoma), cystic lymphangioma or mesothelioma and retroperitoneal haematoma. Making the right diagnosis preoperatively may be often difficult, but MFH may be suspected when a huge retroperitoneal mass is found at imaging in elderly patients. We report a case of a primary abdominal MFH originating from the mesocolon transversum.
原发性恶性纤维组织细胞瘤(MFH)是一种罕见且具有生物学侵袭性的肿瘤。鉴别诊断必须包括胰腺囊性肿瘤(黏液性和浆液性囊腺瘤或囊腺癌)、囊性淋巴管瘤或间皮瘤以及腹膜后血肿。术前做出正确诊断通常可能很困难,但当在影像学检查中发现老年患者有巨大腹膜后肿块时,可能会怀疑为MFH。我们报告一例起源于横结肠系膜的原发性腹部MFH病例。