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因先天性膀胱阴道瘘合并复杂泌尿生殖系统畸形导致的梅努里亚病。

Menouria due to congenital vesicovaginal fistula associated with complex genitourinary malformation.

作者信息

Rajamaheshwari N, Seethalakshmi K, Varghese Lilly

机构信息

Department of Urogynecology, Government Kasturba Gandhi, Hospital, Madras Medical College, Triplicane, Chennai - 600 005, Tamil Nadu, India.

出版信息

Indian J Urol. 2009 Oct-Dec;25(4):534-6. doi: 10.4103/0970-1591.57924.

Abstract

BACKGROUND

Congenital vesicovaginal fistula (VVF) is a very uncommon condition rarely suspected at initial presentation. It is usually seen in association with complex malformations of the genitourinary tract.

CASE

A bifid insertion of the solitary ureter causing an uretero-VVF was associated with an obstructing transverse vaginal septum manifesting as menouria. Also seen were solitary crossed renal ectopia, bicornuate uterus and skeletal anomalies.

CONCLUSION

In women with menouria without vaginal menstruation, pre-operative evaluation to detect an obstructive vaginal anomaly and unusual uretero-vesicovaginal fistulous communications is necessary before surgical intervention.

摘要

背景

先天性膀胱阴道瘘(VVF)是一种非常罕见的疾病,在初次就诊时很少被怀疑。它通常与泌尿生殖道的复杂畸形相关。

病例

单根输尿管的双叉插入导致输尿管-膀胱阴道瘘,并伴有阻塞性阴道横隔,表现为月经血潴留。还发现有孤立性交叉肾异位、双角子宫和骨骼异常。

结论

对于有月经血潴留但无阴道出血的女性,在手术干预前,进行术前评估以检测阻塞性阴道异常和不寻常的输尿管-膀胱阴道瘘沟通是必要的。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4ae5/2808662/72079da37a8e/IJU-25-534-g001.jpg

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