Diller G-P, Baumgartner H
Department of Cardiology and Angiology, Adult Congenital and Valvular Heart Disease Centre (EMAH Zentrum), University Hospital Muenster, University of Muenster, Muenster, Germany.
Int J Clin Pract Suppl. 2010 Jan(165):13-24. doi: 10.1111/j.1742-1241.2009.02244.x.
Pulmonary arterial hypertension (PAH) is a common problem in adult patients with congenital heart disease. We review available data on aetiology, clinical presentation, prognosis and management of PAH in this setting. In addition, we discuss general management strategies and emerging disease-targeting therapies.
肺动脉高压(PAH)是成年先天性心脏病患者的常见问题。我们回顾了这一情况下关于PAH病因、临床表现、预后及管理的现有数据。此外,我们还讨论了一般管理策略和新出现的针对疾病的治疗方法。