一名青春期前儿童的颅内脊索瘤。病例报告。

Intracranial chordoma in a preadolescent. Case report.

作者信息

Oppenheim J S, Rosenblum B R, Sacher M, Wolfe D, Wallace S, Rothman A S

机构信息

Department of Neurosurgery, Mount Sinai Medical Center, New York, New York.

出版信息

Surg Neurol. 1991 Mar;35(3):230-3. doi: 10.1016/0090-3019(91)90076-l.

DOI:10.1016/0090-3019(91)90076-l

PMID:1996453

Abstract

Chordomas are rare tumors derived from notochord remnants occurring primarily in the sacrum, clivus, and cervical regions. Exceptionally, these tumors occur in children, though usually in the sacrum. Eight cases of clivus chordoma have been described in preteenagers. In this report, a clival chordoma with unusual radiologic features is described in an 11-year-old boy. The literature regarding this entity is reviewed.

摘要

脊索瘤是一种罕见的肿瘤，起源于脊索残余组织，主要发生在骶骨、斜坡和颈椎区域。极少数情况下，这些肿瘤也会发生在儿童身上，不过通常是在骶骨部位。此前已有关于青少年斜坡脊索瘤的8例病例报道。在本报告中，描述了一名11岁男孩患有具有不寻常放射学特征的斜坡脊索瘤。本文对有关该疾病的文献进行了综述。