Cooper C, Crolla J A, Laister C, Johnston D I, Cooke P
Department of Cytogenetics, City Hospital, Nottingham.
J Med Genet. 1991 Jan;28(1):6-9. doi: 10.1136/jmg.28.1.6.
We have studied three patients with features of Turner's syndrome, two with a 45,X/46,X,r(?) and the third with a 45,X/46,X,dic?(Y) karyotype. Because Turner's syndrome patients with a mosaic karyotype containing a Y chromosome are known to have a high risk of developing gonadal tumours, we used DNA analysis and in situ hybridisation with X and Y specific probes to identify the chromosomal origin of the rings and dicentric chromosomes in the three index patients. Both ring chromosomes were shown to be of X origin, while the dicentric was composed of Y chromosome material. We discuss the importance of using a combination of molecular and cytogenetic analyses in such cases.
我们研究了三名具有特纳综合征特征的患者,两名患者的核型为45,X/46,X,r(?),第三名患者的核型为45,X/46,X,dic?(Y)。由于已知具有含Y染色体嵌合核型的特纳综合征患者发生性腺肿瘤的风险很高,我们使用DNA分析以及用X和Y特异性探针进行原位杂交,以确定三名索引患者中环状染色体和双着丝粒染色体的染色体来源。两条环状染色体均显示为X染色体来源,而双着丝粒染色体则由Y染色体物质组成。我们讨论了在此类病例中联合使用分子分析和细胞遗传学分析的重要性。