Jedliński Ireneusz, Juszczak Anna, Bugajski Paweł, Kalawski Ryszard, Poprawski Kajetan, Słomczyński Marek
Oddział Kardiologiczny, Szpital im. J. Strusia, Poznań.
Kardiol Pol. 2009 Nov;67(11):1285-6.
Non-compaction myocardium of the left ventricle (LVNC) is a genetically heterogeneous congenital cardiomyopathy characterised by excessive prominent trabeculations and deep intertrabecular recesses which communicate with the left ventricular cavity. Echocardiography plays a pivotal role as a first line diagnostic tool of this rare abnormality. We presented a case of 64-year-old male with LVNC and with papillary muscle involvement.
左心室心肌致密化不全(LVNC)是一种具有遗传异质性的先天性心肌病,其特征为过度突出的小梁和与左心室腔相通的深陷小梁间隐窝。超声心动图作为这种罕见异常的一线诊断工具发挥着关键作用。我们报告了一例64岁男性患有LVNC且累及乳头肌的病例。