University Children's Hospital, Im Neuenheimer Feld 430, 69120 Heidelberg, Germany.
Pediatr Nephrol. 2010 Apr;25(4):659-67. doi: 10.1007/s00467-009-1405-5. Epub 2009 Dec 22.
The post-transplant bone disease of the peripheral skeleton in pediatric renal transplant recipients is characterized by an inadequately thin bone cortex in relation to muscular force. A major hormonal modulator of periosteal growth is the insulin-like growth factor (IGF)/IGF binding protein (IGFBP) system. We therefore hypothesized that the reduced cortical thickness in these patients may be due to functional IGF deficiency. To test this hypothesis, we investigated 55 patients (mean estimated glomerular filtration rate 86.3 +/- 30.0 ml/min/1.73 m(2)) in a cross-sectional study. Parameters of macroscopic bone architecture and forearm muscle size were analyzed by peripheral quantitative computed tomography (pQCT), and serum IGF/IGFBP system components were measured by specific radioimmunoassays. The mean (+/- standard deviation) standardized serum IGF-I (0.20 +/- 1.16 score) level was normal, while the mean IGF-II (1.16 +/- 0.11 score) level was significantly elevated. Serum IGFBP-1 and IGFBP-2 levels were not altered, whereas the IGFBP-3 (1.34 +/- 0.15 score) level was significantly increased. The serum IGFBP-4 level was slightly elevated (by 11%), the IGFBP-6 level was markedly (2.3-fold) elevated, while the IGFBP-5 level was comparable to that of the control. The respective age-adjusted cortical thickness at both the proximal (r = 0.407, P < 0.005) and distal (r = 0.383, P < 0.01) forearm was positively correlated with the standardized serum IGF-I level. In conclusion, the serum IGF/IGFBP system in pediatric renal transplant recipients is characterized by an increase in the levels of the inhibitory IGFBPs, IGFBP-3, -4 and -6, resulting in a functional IGF deficiency. The positive correlation of IGF-I with cortical thickness underlines the importance of this hormonal system in the modeling of bone, particularly periosteal growth.
儿科肾移植受者外周骨骼的移植后骨骼疾病的特征是,皮质骨相对于肌肉力量来说过薄。骨膜生长的主要激素调节剂是胰岛素样生长因子 (IGF)/IGF 结合蛋白 (IGFBP) 系统。因此,我们假设这些患者皮质厚度减少可能是由于 IGF 功能不足。为了验证这一假设,我们在一项横断面研究中调查了 55 名患者(平均估算肾小球滤过率 86.3 +/- 30.0 ml/min/1.73 m(2))。通过外周定量计算机断层扫描 (pQCT) 分析宏观骨结构和前臂肌肉大小的参数,并通过特异性放射免疫分析测量血清 IGF/IGFBP 系统成分。标准化血清 IGF-I(0.20 +/- 1.16 评分)水平的平均值为正常,而 IGF-II(1.16 +/- 0.11 评分)水平显著升高。血清 IGFBP-1 和 IGFBP-2 水平未改变,而 IGFBP-3(1.34 +/- 0.15 评分)水平显著升高。血清 IGFBP-4 水平略有升高(增加 11%),IGFBP-6 水平明显升高(增加 2.3 倍),而 IGFBP-5 水平与对照组相当。近端(r = 0.407,P < 0.005)和远端(r = 0.383,P < 0.01)前臂的年龄调整皮质厚度与标准化血清 IGF-I 水平呈正相关。总之,儿科肾移植受者的血清 IGF/IGFBP 系统的特点是抑制性 IGFBP(IGFBP-3、-4 和 -6)水平升高,导致 IGF 功能不足。IGF-I 与皮质厚度的正相关性强调了该激素系统在骨骼塑造中的重要性,尤其是骨膜生长。