Thabet Ahmed M, Belthur Mohan V, Herzenberg John E
International Center for Limb Lengthening, Rubin Institute for Advanced Orthopedics, Sinai Hospital of Baltimore, Baltimore, Maryland, USA.
J Pediatr Orthop B. 2010 Mar;19(2):161-3. doi: 10.1097/BPB.0b013e3283361b11.
Focal fibrocartilaginous dysplasia (FFCD) is a rare cause of angular deformities around the knee in children. The FFCD lesion most commonly affects the proximal tibia and less commonly the distal femur. We report a case of distal femoral varus deformity secondary to FFCD. Spontaneous resolution of the deformity occurred during a 7-year period. Previous reported femoral cases showed progressive deformity and required treatment with soft-tissue releases with or without osteotomy. This is the first reported femoral case of spontaneous resolution of angular deformity secondary to FFCD. We recommend a trial of observation for distal femoral lesions before surgical intervention.
局灶性纤维软骨发育异常（FFCD）是儿童膝关节周围成角畸形的罕见病因。FFCD病变最常累及胫骨近端，较少累及股骨远端。我们报告1例继发于FFCD的股骨远端内翻畸形病例。该畸形在7年期间自行矫正。既往报道的股骨病例显示畸形进展，需要行软组织松解术，可联合或不联合截骨术治疗。这是首例报道的继发于FFCD的成角畸形自行矫正的股骨病例。我们建议在手术干预前，对股骨远端病变先进行观察。
