Baggett Charles, Skeen Shawn J, Gantt D Scott, Trotter Bradley R, Birkemeier Krista L
Department of Internal Medicine, Scott & White Hospital, Texas A&M Health Science Center College of Medicine, Temple, Texas 76508, USA.
Tex Heart Inst J. 2009;36(6):611-4.
Isolated right superior vena cava drainage into the left atrium is an extremely rare cardiac anomaly, especially in the absence of other cardiac abnormalities. Only 28 of 5,127 reported consecutive congenital cardiac cases involved superior vena cava drainage into the left atrium, and all were associated with other cardiac anomalies. Of 19 reported cases of right superior vena cava drainage into the left atrium, most patients have been children who were experiencing mild hypoxemia and cyanosis. Herein, we describe the case of a 34-year-old woman who presented with asymptomatic hypoxemia in the peripartum period. She was diagnosed to have isolated drainage of the right superior vena cava into the left atrium. To the best of our knowledge, this is the 1st reported instance of such diagnosis by use of noninvasive imaging only, without cardiac catheterization. We also review the medical literature that pertains to our patient's anomaly.
孤立的右上腔静脉引流至左心房是一种极其罕见的心脏异常，尤其是在没有其他心脏异常的情况下。在连续报告的5127例先天性心脏病病例中，只有28例涉及上腔静脉引流至左心房，并且所有病例都伴有其他心脏异常。在报告的19例右上腔静脉引流至左心房的病例中，大多数患者为儿童，表现为轻度低氧血症和发绀。在此，我们描述了一名34岁女性，她在围产期出现无症状性低氧血症。她被诊断为孤立的右上腔静脉引流至左心房。据我们所知，这是首次仅通过无创成像而非心导管检查做出此类诊断的报告实例。我们还回顾了与我们患者的异常情况相关的医学文献。
