Williams Matthew L, Wechsler Stephanie Burns, Hughes G Chad
Division of Thoracic and Cardiovascular Surgery, Department of Surgery, Duke University, Durham, North Carolina.
J Card Surg. 2010 Jan 7. doi: 10.1111/j.1540-8191.2010.00956.x.
Abstract Loeys-Dietz syndrome (LDS) is a recently described connective tissue disorder characterized by generalized arterial tortuosity and aggressive aortopathy that untreated leads to early death even at aortic dimensions as small as 4 cm. We report the case of a young man with LDS successfully treated for aortic root, arch, and thoracoabdominal pathology.(J Card Surg ****;:-**).