用于洛伊斯-迪茨综合征的两阶段全主动脉置换术。
Two-stage total aortic replacement for Loeys-Dietz syndrome.
作者信息
Williams Matthew L, Wechsler Stephanie Burns, Hughes G Chad
机构信息
Division of Thoracic and Cardiovascular Surgery, Department of Surgery, Duke University, Durham, North Carolina 27710, USA.
出版信息
J Card Surg. 2010 Mar;25(2):223-4. doi: 10.1111/j.1540-8191.2009.00956.x.
Abstract
Loeys-Dietz syndrome (LDS) is a recently described connective tissue disorder characterized by generalized arterial tortuosity and aggressive aortopathy that untreated leads to early death even at aortic dimensions as small as 4 cm. We report the case of a young man with LDS successfully treated for aortic root, arch, and thoracoabdominal pathology.
摘要
洛伊迪茨综合征（LDS）是一种最近才被描述的结缔组织疾病，其特征为全身性动脉迂曲和侵袭性主动脉病变，未经治疗即使在主动脉直径小至4厘米时也会导致早期死亡。我们报告了一例患有LDS的年轻男性，其主动脉根部、主动脉弓及胸腹段病变均得到成功治疗。
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