Department of Neurosurgery, West China Hospital, Sichuan University, Chengdu wai nan guo xue xiang 37#, Chengdu, Sichuan 610041, China.
J Clin Neurosci. 2010 Mar;17(3):402-3. doi: 10.1016/j.jocn.2009.05.017. Epub 2010 Jan 13.
We report a 51-year-old man with an unusual intradural suprasellar chondroid chordoma. He presented with headache and diminution of vision in both eyes. MRI demonstrated the suprasellar tumor as an isointense mass with heterogeneous enhancement after intravenous administration of contrast agent. There was neither bony nor dural association, and gross-total removal of the mass was performed using a left extended pterional approach. Based on the histological characteristics of the tumor, which was composed of typical chordoma cells and islands of chondroid elements, we diagnosed a chondroid chordoma. We believe this is the first report of an entirely intradural chondroid chordoma on the suprasellar region. Clinical, radiological, and pathological features of the tumor are described.
我们报告一例 51 岁男性颅内脊索瘤。他表现为头痛和双眼视力下降。MRI 显示鞍上肿瘤为等信号肿块,静脉注射造影剂后呈不均匀强化。既无骨也无脑膜附着,使用左扩大翼点入路行大体全切除。基于肿瘤的组织学特征,由典型脊索瘤细胞和软骨样成分岛组成,我们诊断为软骨脊索瘤。我们认为这是首例发生于鞍上完全颅内脊索瘤的报告。描述了肿瘤的临床、放射学和病理学特征。