Clival dysgenesis associated with Chiari Type 1 malformation and syringomyelia.

We report an 11-year-old boy with dysgenesis of the clivus. The boy presented complaining of progressive difficulty in walking. The clival anomaly was associated with severe basilar invagination, Chiari Type 1 malformation and syringomyelia. Our literature search did not reveal any previous reports of this combination of conditions. The patient obtained relief from his symptoms following a foramen magnum decompression.