Type 2 segmental Darier's disease in a twelve-year-old Nigerian male--a case report.

Darier's disease is an autosomal dominant disorder characterized clinically by presence of keratotic papules in a seborrheic distribution, nail involvement and mucosal lesions. There are several clinical variants of Darier's disease, but few cases of segmental Darier's disease have been described in the literature. We describe a 12-year-old boy with type 2 mosaic phenotype. This unique clinical variant of Darier's disease has been described very rarely.