Department of Medical Imaging, Chun Shan Medical University Hospital, Taichung, Taiwan.
Clin Imaging. 2010 Jan-Feb;34(1):57-9. doi: 10.1016/j.clinimag.2009.03.005.
A young woman with type 1 neurofibromatosis (NF-1) complained of abdominal pain for 3 days. Computed tomography disclosed two jejunal tumors with rupture and peritonitis. Surgery revealed two tumors in the jejunum, one of which was ruptured. Specimen examination found four additional intramural nodules between these tumors. Histology proved these tumors were all gastrointestinal stromal tumors (GIST). The finding of multiple digestive tumors associated with peritonitis in an NF-1 patient should lead to the consideration of a ruptured GIST.
一位患有 1 型神经纤维瘤病（NF-1）的年轻女性诉腹痛 3 天。计算机断层扫描显示两段空肠肿瘤破裂伴腹膜炎。手术显示两段空肠各有一个肿瘤，其中一个破裂。标本检查发现这两个肿瘤之间还有四个额外的壁内结节。组织学证实这些肿瘤均为胃肠道间质瘤（GIST）。NF-1 患者伴腹膜炎的多个消化道肿瘤的发现应考虑为破裂的 GIST。
