Vermeulen Tom, Conraads Viviane M, Vrints Christiaan, Rodrigus Inez E
Department of Cardiology, Antwerp University Hospital, Belgium.
Acta Cardiol. 2009 Dec;64(6):811-4. doi: 10.2143/AC.64.6.2044749.
Myxoma cordis is the most frequent primary cardiac tumour in adults. Paediatric primary cardiac tumours are rare, the most common type being rhabdomyoma. Atrial and ventricular myxomas occur infrequently in the paediatric age group. Intracardiac myxomas are seen with an estimated incidence of 0.5 per million population per year. Approximately 70% of the affected patients are of female gender. Recurrences are rare (1.3%). Asymptomatic recurrences are observed in young patients who have a familial history of tumour or multifocal myxomas. Although rare, cardiac aetiology (atrial fibrillation, intracardiac thrombi, patent foramen ovale, myxoma, endocarditis) should be considered. In children presenting with central neurological symptoms, a cardiac aetiology has to be considered. We describe a rare case of an 18-year-old girl presenting with a recurrent left ventricular myxoma, accompanied by neurological deficits.
心脏黏液瘤是成人中最常见的原发性心脏肿瘤。小儿原发性心脏肿瘤罕见,最常见的类型是横纹肌瘤。心房和心室黏液瘤在儿童年龄组中很少见。心脏内黏液瘤的年发病率估计为每百万人口0.5例。约70%的患病患者为女性。复发很少见(1.3%)。在有肿瘤家族史或多灶性黏液瘤的年轻患者中观察到无症状复发。虽然罕见,但应考虑心脏病因(心房颤动、心内血栓、卵圆孔未闭、黏液瘤、心内膜炎)。对于出现中枢神经系统症状的儿童,必须考虑心脏病因。我们描述了一例罕见的18岁女孩复发性左心室黏液瘤伴神经功能缺损的病例。