Department of Orthopedic Surgery, Uijeongbu St Mary's Hospital, The Catholic University of Korea, Uijeongbu, Korea.
Skeletal Radiol. 2010 Jun;39(6):595-600. doi: 10.1007/s00256-009-0872-x. Epub 2010 Feb 12.
Extraskeletal Ewing's sarcoma (ES) and primitive neuroectodermal tumor (PNET) are widely regarded as clinically and histologically identical tumors which consist of small blue round cells. Extraskeletal ESs/PNETs usually occur in the deep soft tissues of the paraspinal region, chest wall, or lower extremities. However, superficially located cases, so-called cutaneous ESs/PNETs, are exceedingly rare, and the vast majority of the reported cases present as a single small mass. We present magnetic resonance imaging (MRI) findings and clinical course of a unique case of primary cutaneous ES/PNET presenting as numerous huge masses with severe ulceration on them.
骨外尤文氏肉瘤(ES)和原始神经外胚层肿瘤(PNET)被广泛认为是临床上和组织学上相同的肿瘤,由小的蓝色圆形细胞组成。骨外 ES/PNET 通常发生在脊柱旁区域、胸壁或下肢的深部软组织中。然而,位于表面的病例,即所谓的皮肤 ES/PNET,极为罕见,绝大多数报道的病例表现为单个小肿块。我们报告了一个独特的原发性皮肤 ES/PNET 病例的磁共振成像(MRI)表现和临床过程,该病例表现为数个巨大肿块,伴有严重溃疡。