Institute of Otorhinolaryngology and Head and Neck Surgery, Azienda Ospedaliera S.Maria, via Tristano di Joannuccio, Terni, Italy.
Acta Otorhinolaryngol Ital. 2009 Aug;29(4):218-21.
The authors present a case of heterotopic central nervous system tissue observed in an 81-year-old male in the form of an ethmoidal polyp. A review of the literature indicates that this is a rare condition characterised by a connective tissue lesion with astrocytic and oligodendrocytic glial cells, which may be located outside the nasal pyramid in some cases and inside the nasal cavity in others. The most important diagnostic aspect involves differentiating these from meningoencephalocele, which maintains an anatomical connection with central nervous system tissue. Contrast-enhanced imaging is essential for diagnosis, as in cases of heterotopic central nervous system tissue, it will demonstrate that there are no connections with intra-cranial tissue. Endoscopic excision is the treatment of choice.
作者报告了一例 81 岁男性鼻腔内以筛状息肉形式存在的中枢神经系统组织异位病例。文献复习表明,这是一种罕见的疾病,其特征为具有星形胶质细胞和少突胶质细胞的结缔组织病变,在某些情况下可能位于鼻锥外,在其他情况下位于鼻腔内。最重要的诊断方面是将其与脑膜脑膨出区分开来,后者与中枢神经系统组织保持解剖学连接。增强对比成像对于诊断至关重要,因为在中枢神经系统组织异位的情况下,它将表明与颅内组织没有连接。内镜切除是首选的治疗方法。