Delbouck C, Roper N, Aubert C, Souchay C, Choufani G, Hassid S
ENT Department, Hôpital Erasme, Université Libre de Bruxelles, Belgium.
B-ENT. 2009;5(4):265-8.
Unusual presentation of adenoid cystic carcinoma of the maxillary antrum. Adenoid cystic carcinoma (ACC) is a rare tumour which affects mainly the major and accessory salivary glands. It is an aggressive neoplasm characterized by early neural invasion and a high incidence of local recurrence and distant metastases, which may develop years after the initial resection. Surgery followed by radiotherapy seems to be the best treatment. Based on a well-illustrated case of extensive maxillary ACC involving the palate, orbit floor, and pterygo-palatine fossa, we discuss the prognosis and the importance of an early diagnosis of ACC.
上颌窦腺样囊性癌的罕见表现。腺样囊性癌（ACC）是一种罕见肿瘤，主要累及大唾液腺和小唾液腺。它是一种侵袭性肿瘤，其特征为早期神经侵犯以及局部复发和远处转移的高发生率，远处转移可能在初次切除数年之后发生。手术联合放疗似乎是最佳治疗方法。基于一例累及腭部、眶底和翼腭窝的广泛上颌窦腺样囊性癌的详细病例，我们讨论腺样囊性癌的预后及早期诊断的重要性。
