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腹茧症。病例报告。

The abdominal cocoon. A case report.

作者信息

Reynders D, Van der Stighelen Y

机构信息

Department of General Surgery, St. Vincentius Hospital Antwerp, Belgium.

出版信息

Acta Chir Belg. 2009 Nov-Dec;109(6):772-4. doi: 10.1080/00015458.2009.11680534.

Abstract

The abdominal cocoon, or idiopathic sclerosing encapsulating peritonitis, is a rare cause of intestinal obstruction. This rare condition, in which the small intestine is encased in a thick fibrous membrane, has been reported predominantly in females. Despite some reports of a preoperative diagnosis, in the majority of cases diagnosis is only made at laparotomy for acute or subacute intestinal obstruction. Treatment consists of resection of the membrane with lysis of adhesions. We present a case of abdominal cocoon in a man where early preoperative diagnosis by radiological evaluation was overlooked. A better awareness of this condition may result in early diagnosis and proper management, thus avoiding unnecessary bowel resections and bad outcomes.

摘要

腹茧症,即特发性硬化性包裹性腹膜炎,是肠梗阻的罕见病因。这种罕见病症中,小肠被一层厚厚的纤维膜包裹,主要见于女性。尽管有一些术前诊断的报道,但大多数病例仅在因急性或亚急性肠梗阻行剖腹手术时才得以确诊。治疗方法包括切除纤维膜并松解粘连。我们报告一例男性腹茧症病例,该病例经影像学评估的早期术前诊断被忽视。对这种病症有更深入的认识可能会实现早期诊断和恰当处理,从而避免不必要的肠切除及不良后果。

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引用本文的文献

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