Darbi A, Cenoui F, Atmane A, Amil T, Hanine A
Service d'imagerie, hôpital militaire d'instruction Mohammed V, Hay Ryad, Rabat, Maroc.
Arch Pediatr. 2010 Apr;17(4):378-82. doi: 10.1016/j.arcped.2010.01.005. Epub 2010 Feb 26.
Cochleovestibular dysplasia or Mondini malformation is exceptional. Cochlear dysplasia is due to early cessation of the development of the inner ear during embryonic life. We report on the case of an infant who presented with perception deafness and repeated meningitis. CT allowed the diagnosis of Mondini malformation. We underline the importance of high-resolution CT in the diagnosis of Mondini malformation.
耳蜗前庭发育异常或Mondini畸形较为罕见。耳蜗发育异常是由于胚胎期内耳发育过早停止所致。我们报告了一例表现为感音神经性耳聋和反复脑膜炎的婴儿病例。CT检查确诊为Mondini畸形。我们强调高分辨率CT在Mondini畸形诊断中的重要性。
