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经胸超声心动图检查中被忽视的诊断:心尖肥厚型心肌病。

An overlooked diagnosis on transthoracic echocardiography: apical hypertrophic cardiomyopathy.

作者信息

Yiğiner Omer, Cingözbay Bekir Yilmaz, Uz Omer, Cebeci Bekir Sitki

机构信息

Department of Cardiology, Haydarpaşa Training Hospital, Gülhane Military Medical Academy, Istanbul, Turkey.

出版信息

Turk Kardiyol Dern Ars. 2009 Dec;37(8):569-71.

Abstract

Apical hypertrophic cardiomyopathy (HCM) may be overlooked during routine echocardiography. A 54-year-old male patient with dyslipidemia and positive family history presented with atypical chest pain. The 12-lead electrocardiogram showed increased QRS voltage and deep T-wave inversions in precordial leads. Transthoracic echocardiography performed with poor echocardiographic windows demonstrated normal findings. Coronary angiography showed normal coronary arteries. Left ventriculography revealed a spade-like deformity (ace of spades), typical for apical HCM. Cardiac magnetic resonance imaging confirmed the diagnosis.

摘要

肥厚型心肌病(HCM)的心尖肥厚型在常规超声心动图检查时可能会被漏诊。一名54岁男性患者,有血脂异常且家族史阳性,出现非典型胸痛。12导联心电图显示胸前导联QRS电压增高及T波深倒置。经胸超声心动图检查时超声窗欠佳,结果显示正常。冠状动脉造影显示冠状动脉正常。左心室造影显示典型的心尖肥厚型心肌病的黑桃样畸形(黑桃A)。心脏磁共振成像确诊了该病。

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