Ucak Alper, Onan Burak, Inan Kaan, Ugur Murat, Kucukodaci Zafer, Yilmaz Ahmet Turan
Department of Cardiovascular Surgery, GATA Haydarpasa Education Hospital, Istanbul, Turkey.
J Card Surg. 2010 May;25(3):347-9. doi: 10.1111/j.1540-8191.2010.01004.x. Epub 2010 Feb 23.
Endocardial fibroelastosis is characterized by massive proliferation of collagenous and elastic tissue, in which the pathological process is restricted to the endocardium. In this report, we present the case of a 20-year-old man with Behcet's disease and endocardial fibroelastosis of the right ventricle involving tricuspid valve resulting in a tumor mass that was resected along with tricuspid valve replacement. The clinical and pathological features of this rare entity are reviewed.
心内膜弹力纤维增生症的特征是胶原组织和弹性组织大量增生，其病理过程局限于心内膜。在本报告中，我们介绍了一名20岁男性白塞病患者的病例，该患者右心室心内膜弹力纤维增生症累及三尖瓣，导致肿瘤样肿物，该肿物与三尖瓣置换一并切除。本文对这一罕见疾病的临床和病理特征进行了综述。
