Division of Gastroenterology and Hepatology, Department of Medicine, Washington Hospital Center, Washington, DC 20010, USA.
J Clin Gastroenterol. 2010 Jul;44(6):428-31. doi: 10.1097/MCG.0b013e3181d476fc.
Fifty years ago, only a quarter of infants born with congenital heart disease (CHD) survived beyond the first year of life. It has been estimated that 80% to 85% of patients can expect to reach adulthood. Today, there are close to 1 million adults living with CHD in the United States alone. Since its introduction, the Fontan operation has become established as the dominant surgical repair in patients with univentricular heart physiology. Long-term morbidity associated with this procedure is being more commonly appreciated and liver complications have become more frequently apparent. Hepatologist awareness and familiarity in managing this population alongside the CHD specialist is important for the care of these patients. This dual perspective can provide comprehensive integrated care.
五十年前，只有四分之一患有先天性心脏病 (CHD) 的婴儿能活过一岁。据估计，80% 到 85% 的患者可以活到成年。如今，仅在美国就有近 100 万成年人患有 CHD。自引入以来，Fontan 手术已成为单心室心脏生理患者的主要手术修复方法。人们越来越认识到该手术相关的长期发病率，并且肝脏并发症也越来越常见。肝科医生在与 CHD 专家一起管理该人群方面的意识和熟悉程度对于这些患者的护理非常重要。这种双重观点可以提供全面的综合护理。
