Zannad Noura, Pierre Bertrand, Cosnay Pierre, Babuty Dominique
Hôpital Trousseau, Cardiology, Tours, France.
Pacing Clin Electrophysiol. 2010 May;33(5):618-9. doi: 10.1111/j.1540-8159.2010.02696.x. Epub 2010 Mar 8.
We report the case of an 18-year-old man with Danon disease, a genetic disorder inclunding a severe hypertrophic cardiomyopathy with very broad QRS, who had an implantable cardioverter defibrillator for primary prevention. Nine months after implantation, he received two inappropriate shocks due to R-wave double counting during sinus tachycardia. We discuss how to avoid such inappropriate therapy.
我们报告了一例18岁患有丹侬病的男性病例,丹侬病是一种遗传性疾病,包括严重的肥厚型心肌病且QRS波极宽,该患者植入了植入式心律转复除颤器用于一级预防。植入后九个月,他在窦性心动过速期间因R波双重计数而接受了两次不适当的电击。我们讨论了如何避免这种不适当的治疗。