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4-Hydroxybutyric aciduria: application of a fluorometric assay to the determination of succinic semialdehyde dehydrogenase activity in extracts of cultured human lymphoblasts.

作者信息

Gibson K M, Lee C F, Chambliss K L, Kamali V, Francois B, Jaeken J, Jakobs C

出版信息

Clin Chim Acta. 1991 Feb 15;196(2-3):219-21. doi: 10.1016/0009-8981(91)90076-o.

DOI:10.1016/0009-8981(91)90076-o
PMID:2029787
Abstract
摘要

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4-Hydroxybutyric aciduria: application of a fluorometric assay to the determination of succinic semialdehyde dehydrogenase activity in extracts of cultured human lymphoblasts.4-羟基丁酸尿症：荧光测定法在测定培养的人淋巴母细胞提取物中琥珀酸半醛脱氢酶活性的应用。
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[4-Hydroxybutyric aciduria].[4-羟基丁酸尿症]
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