Department of Pediatric Urology, Schneider's Children Hospital, New Hyde Park, New York, USA.
J Plast Reconstr Aesthet Surg. 2010 Dec;63(12):2141-5. doi: 10.1016/j.bjps.2010.02.005. Epub 2010 Mar 29.
Genital anomalies in females born with classic bladder exstrophy-epispadias complex (EEC) include a bifid clitoris and anterior displacement of vagina. The aesthetic aspects of the genitals acquire greater significance with age and may affect self-esteem. We review our experience with clitoral reconstruction in an EEC population with an emphasis on aesthetic outcomes.
The study group had 26 female patients; three patients with isolated epispadias and 23 with bladder exstrophy. The patients were separated into four separate groups based on reconstructive technique. Group 1 (n=3) had tubularisation of skin between clitoral bodies for urethral reconstruction; group 2 (n=12) underwent staged exstrophy reconstruction; group 3 (n=8) had initial surgery elsewhere and were referred for secondary reconstructive surgery with clitoroplasty accompanied by puboplasty to reconstruct the fourchette; and group 4 (n=3) had total urogenital sinus mobilisation. The aesthetic outcome was assessed subjectively by the surgeon, parent and age-appropriate patient during follow-up.
A total of 33 clitoroplasties were performed. Primary clitoroplasty was performed in 18 patients, while a secondary clitoroplasty was done in 15. The follow-up ranged from 3 months to 31 years. Three patients had partial clitoral atrophy and in one patient the gap between clitoral bodies was widely separated and incapable of being joined. Twenty-three of the26 patients (88%) had a satisfactory or excellent aesthetic outcome following clitoroplasty.
Excellent aesthetic outcomes can be achieved by clitoroplasty in EEC patients by using a variety of surgical techniques. We recommend a 'second look' reassessment near puberty to identify poor cosmesis and offer secondary clitoroplasty to improve aesthetic outcome.
患有经典膀胱外翻-尿道上裂复合畸形(EEC)的女性出生时存在生殖器畸形,包括阴蒂分叉和阴道前移位。随着年龄的增长,生殖器的美学方面变得更加重要,可能会影响自尊心。我们回顾了在 EEC 人群中进行阴蒂重建的经验,重点关注美学结果。
研究组有 26 名女性患者;3 名患者单纯患有尿道上裂,23 名患者患有膀胱外翻。根据重建技术将患者分为四组。第 1 组(n=3)采用阴蒂体之间的皮肤管状化进行尿道重建;第 2 组(n=12)接受分期外翻重建;第 3 组(n=8)在其他地方接受初始手术,然后进行二次重建手术,同时进行阴蒂成形术和耻骨成形术,以重建阴蒂系带;第 4 组(n=3)行全尿生殖窦游离术。在随访过程中,由外科医生、家长和年龄适当的患者对美学结果进行主观评估。
共进行了 33 次阴蒂成形术。18 例患者行一期阴蒂成形术,15 例患者行二期阴蒂成形术。随访时间为 3 个月至 31 年。3 例患者出现部分阴蒂萎缩,1 例患者阴蒂体之间的间隙分离较大,无法连接。26 例患者中的 23 例(88%)经阴蒂成形术后获得满意或优秀的美学效果。
通过使用多种手术技术,EEC 患者可以通过阴蒂成形术获得极佳的美学效果。我们建议在接近青春期时进行“二次观察”评估,以识别不良美容效果,并提供二次阴蒂成形术以改善美学效果。