Hulselmans Michael, Benit Edouard
Dept. of Cardiology, Virga Jesse Hospital, Hasselt, Belgium.
Acta Cardiol. 2010 Feb;65(1):89-92. doi: 10.2143/AC.65.1.2045896.
We present the case of a patient with Noonan syndrome who was seen for the first time at the age of 69 years with combined pulmonary valve stenosis and atrial septal defect. The patient was treated by a staged percutaneous approach. The treatment of these combined congenital heart defects remains challenging because their haemodynamics interact directly. In this case report we discuss both the underlying pathophysiology and haemodynamics.
我们报告一例努南综合征患者,该患者69岁首次就诊,患有肺动脉瓣狭窄合并房间隔缺损。患者接受了分期经皮治疗。这些先天性心脏病合并症的治疗仍然具有挑战性,因为它们的血流动力学直接相互作用。在本病例报告中,我们讨论了潜在的病理生理学和血流动力学。