Nuebel Julia, Januszewska Katarzyna, Loeff Markus, Theisen Daniel, Malec Edward, Dalla-Pozza Robert
Pediatric Cardiology and Intensive Care, Ludwig-Maximilians-University, Munich, Germany.
J Cardiothorac Surg. 2010 Mar 25;5:15. doi: 10.1186/1749-8090-5-15.
Scimitar syndrome is a rare congenital anomaly characterized by total or partial anomalous pulmonary venous drainage of the right lung to the inferior vena cava. We present a seven year old girl with a systolic murmur who was diagnosed as having a Scimitar syndrome with unusual drainage of the right pulmonary veins. The unique technique of surgery in this patient was appropriate to the unusual, previously not described anatomy.
弯刀综合征是一种罕见的先天性异常,其特征为右肺全部或部分肺静脉异常引流至下腔静脉。我们报告一名7岁女童,有收缩期杂音,被诊断为弯刀综合征,伴有右肺静脉异常引流。该患者独特的手术技术适合其异常的、此前未描述过的解剖结构。