Pawar Ravindra S, Raj Vimal, Pujar V Suresh
1Department of Pediatric Cardiology,Narayana Institute of Cardiac Sciences,Bangalore,Karnataka,India.
2Department of Radiodiagnosis and Imaging,Majumdar Shaw Medical Centre,Narayana Health City,Bangalore,Karnataka,India.
Cardiol Young. 2018 Oct;28(10):1171-1173. doi: 10.1017/S1047951118001117. Epub 2018 Jul 11.
Scimitar or pulmonary venolobar syndrome, a rare pulmonary anomaly, consists basically of anomalous pulmonary venous drainage of the right lung to the inferior caval vein, anomalous systemic arterial supply to the right lower lobe from the descending aorta, hypoplasia of the right lung, and dextroposed heart. We present a rare case with constellation of all these findings of scimitar syndrome, but with the aberrant pulmonary vein draining into the left atrium.
弯刀综合征或肺静脉叶综合征是一种罕见的肺部异常，主要包括右肺肺静脉异常引流至下腔静脉、降主动脉向右下叶提供异常的体循环动脉供血、右肺发育不全以及心脏右位。我们报告一例罕见病例，具备弯刀综合征的所有这些表现，但异常肺静脉引流至左心房。
