Cardiac Surgical Associates of Florida, Orlando, Florida 34741, USA.
Ann Thorac Surg. 2010 Apr;89(4):1283-4. doi: 10.1016/j.athoracsur.2009.08.076.
Noncompaction of the left ventricle is a rare congenital cardiomyopathy characterized by prematurely arrested compaction of the endocardial and myocardial fibers. Although systolic heart failure is assured, treatment has been traditionally limited to palliative medical therapy or transplantation. We present the first report of long-term clinical and echocardiographic follow-up (50 months) showing sustained myocardial recovery after the use of mitral valve annuloplasty as the primary treatment for severe mitral regurgitation associated with left ventricular noncompaction.
左心室心肌致密化不全是一种罕见的先天性心肌病，其特征是心内膜和心肌纤维过早停止致密化。尽管收缩性心力衰竭是不可避免的，但传统上的治疗方法仅限于姑息性药物治疗或移植。我们首次报道了长期临床和超声心动图随访（50 个月），显示在二尖瓣瓣环成形术作为原发性治疗严重二尖瓣反流伴左心室心肌致密化不全后，心肌持续恢复。
