Renu Divya, Rao B Ganesh, Ranganath K
Department of Radiodiagnosis, RAGAVS Diagnostic and Research Centre Pvt Ltd, Sadguru Complex, No.14, 27 Cross, 4 Block West, Jayanagar, Bangalore - 560 011, India.
Indian J Radiol Imaging. 2010 Feb;20(1):72-4. doi: 10.4103/0971-3026.59761.
Persistent Mullerian duct syndrome (PMDS) is a rare form of internal male pseudohermaphroditism in which Mullerian duct derivatives are seen in a male patient. This syndrome is characterized by the persistence of Mullerian duct derivatives (i.e. uterus, cervix, fallopian tubes and upper two thirds of vagina) in a phenotypically and karyotypically male patient. In this article we present the USG and MRI features of a case of PMDS with bilateral cryptorchidism and left sided inguinal hernia, containing the uterus and fallopian tubes.
持续性苗勒管综合征(PMDS)是一种罕见的男性内部假两性畸形,在男性患者中可见苗勒管衍生物。该综合征的特征是在表型和核型均为男性的患者中,苗勒管衍生物(即子宫、宫颈、输卵管和阴道上三分之二)持续存在。在本文中,我们展示了一例伴有双侧隐睾和左侧腹股沟疝(疝内容物为子宫和输卵管)的PMDS患者的超声和磁共振成像特征。