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左心室心肌致密化不全合并支气管扩张症,继发AA型淀粉样变性并累及肾脏

[Left ventricular noncompaction concurrent with bronchoectatic disease complicated by secondary AA-amyloidosis with renal involvement].

作者信息

Fomin V V, Rameev V V, Sedov V P, Severova M M, Svet A V, Miroshnichenko N G, Kozlovskaia L V

出版信息

Ter Arkh. 2010;82(1):73-7.

PMID:20364708
Abstract

The paper describes a clinical case of congenital cardiomyopathy (left ventricular noncompaction) concurrent with secondary amyloidosis and renal involvement that develops at the outcome of long existing brochoectatic disease.

摘要

本文描述了一例先天性心肌病(左心室心肌致密化不全)合并继发性淀粉样变性和肾脏受累的临床病例,该病例是在长期存在的支气管扩张症的基础上发生的。

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Ter Arkh. 2010;82(1):73-7.
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