Fomin V V, Rameev V V, Sedov V P, Severova M M, Svet A V, Miroshnichenko N G, Kozlovskaia L V
Ter Arkh. 2010;82(1):73-7.
The paper describes a clinical case of congenital cardiomyopathy (left ventricular noncompaction) concurrent with secondary amyloidosis and renal involvement that develops at the outcome of long existing brochoectatic disease.
本文描述了一例先天性心肌病(左心室心肌致密化不全)合并继发性淀粉样变性和肾脏受累的临床病例,该病例是在长期存在的支气管扩张症的基础上发生的。