Berardi R S, Korba J, Melton J, Chen H
Surgical Department, VA Medical Center, Des Moines, Iowa, 50310.
Int Surg. 1991 Jan-Mar;76(1):64-6.
Nevoid basal cell carcinoma syndrome is a relatively uncommon clinical entity. It is essentially characterized by the early onset of multiple basal cell carcinomas of the skin generally above wrist-line level, by the presence of jaw cysts, musculoskeletal and other anomalies. Metastatic disease secondary to ordinary basal cell carcinoma is indeed rare. What is even more rare is pulmonary metastases from basal cell carcinoma. Very few cases have been reported in which pulmonary resection was performed for metastatic basal cell carcinoma. We were unable to find a reported case in which pulmonary resection was performed for a pulmonary nodule metastatic from the nevoid basal cell carcinoma syndrome. Herein is reported what we believe to be the first case of pulmonary resection performed for a metastatic nodule in this syndrome.
痣样基底细胞癌综合征是一种相对罕见的临床病症。其基本特征为皮肤多发基底细胞癌通常在腕部以上水平早期发病，伴有颌骨囊肿、肌肉骨骼及其他异常。普通基底细胞癌继发的转移性疾病确实罕见。更罕见的是基底细胞癌的肺转移。报道中极少有因转移性基底细胞癌而行肺切除术的病例。我们未能找到因痣样基底细胞癌综合征转移至肺部的结节而行肺切除术的报道病例。本文报道了我们认为的该综合征中首例因转移性结节而行肺切除术的病例。
