Department of Thrombosis and Haemostasis, Guy's & St. Thomas' Hospital, London, UK.
Br J Haematol. 2010 Jun;149(6):813-23. doi: 10.1111/j.1365-2141.2010.08191.x. Epub 2010 Apr 29.
Severe platelet function defects are rare disorders that require expertise in diagnosis and management. Therefore patients with such disorders should be referred to and managed in centres with the full laboratory repertoire of tests and clinical support necessary to optimise their quality of care. The aim of this review is to discuss the management of these patients in various clinical situations including surgical intervention.
严重的血小板功能缺陷是罕见疾病,需要在诊断和管理方面具有专业知识。因此,此类疾病患者应转诊至具有全套实验室检测和必要临床支持的中心进行管理,以优化其护理质量。本文的目的是讨论这些患者在各种临床情况下(包括手术干预)的管理。