Swanson Edward W, Matros Evan, Perez-Atayde Antonio R, Mulliken John B
Department of Plastic Surgery, Children's Hospital Boston and Harvard Medical School, Boston, Massachusetts 02115, USA.
J Craniofac Surg. 2010 May;21(3):866-9. doi: 10.1097/SCS.0b013e3181d7f1ea.
Facial dermoids are uncommon. We present the first case of a nasomaxillary dermoid since Bramann's original 1890 description. A dermoid sinus in this location further supports Bland-Sutton's hypothesis of ectodermal sequestration between embryologic facial prominences. Contralateral cleft lip and palate in our patient suggest a common pathogenesis involving abnormal formation of the maxillary prominences and failure of fusion and merging.
面部皮样囊肿并不常见。自1890年布拉曼首次描述以来,我们首次报告了一例鼻上颌皮样囊肿病例。该部位的皮样窦进一步支持了布兰德 - 萨顿关于胚胎面部隆起之间外胚层隔离的假说。我们患者的对侧唇腭裂提示存在一种共同的发病机制,涉及上颌隆起的异常形成以及融合和合并失败。