Department of Experimental Medicine, "Sapienza" University, Viale Regina Elena, 324, 00161, Rome, Italy.
Clin Rev Allergy Immunol. 2011 Jun;40(3):170-80. doi: 10.1007/s12016-010-8207-1.
The spectrum of morphologic changes in lupus nephritis, either microscopic, ultrastructural, or immunohistological, closely reflects the great variety of immune complexes that are produced in the course of the disease. Every tissue component of the kidney can be affected, but glomeruli are the target structure in most patients. Several attempts have been made to correlate the clinical severity and the outcome of the nephritis with the pathologic features; the current classification and the six classes that resulted from an international study group are entirely based on glomerular changes. Major criteria of classification include the focal or diffuse involvement of the glomerulus, the site of hypercellularity, the site of immune complex deposition and the presence of active and/or sclerotic lesions. Even if less thoroughly investigated than the glomerulus, the interstitial compartment has revealed many interesting features as are vascular lesions, a common and often underestimated feature. Typing of subpopulation of lymphoid infiltrates supports the emerging evidence indicating that B cells are promoting autoimmunity in mechanisms other than autoAb secretion. Many aspects are still debated and/or poorly understood, such as the interpretation of the so-called "full house nephropathy" that closely mimic lupus nephritis in seronegative patients.
狼疮肾炎的形态学变化范围,无论是微观、超微结构还是免疫组织化学,都紧密反映了在疾病过程中产生的大量免疫复合物。肾脏的每一种组织成分都可能受到影响,但肾小球是大多数患者的靶结构。人们曾多次尝试将肾炎的临床严重程度和预后与病理特征相关联;目前的分类和一个国际研究小组得出的六个分类完全基于肾小球的变化。分类的主要标准包括肾小球的局灶性或弥漫性受累、细胞增生的部位、免疫复合物沉积的部位以及活动和/或硬化病变的存在。即使不如肾小球那样被深入研究,间质腔也揭示了许多有趣的特征,如血管病变,这是一种常见且经常被低估的特征。淋巴细胞浸润亚群的分型支持了正在出现的证据,表明 B 细胞在除自身抗体分泌之外的机制中促进自身免疫。许多方面仍存在争议和/或理解不足,例如对所谓的“满堂肾病”的解释,这种疾病在血清阴性患者中与狼疮肾炎非常相似。